ELISA Alpha galactosidase A anti-
Quantity:100µg
Purification:Immunogen affinity purified
Form:liquid
Purity:?95% as determined by SDS-PAGE
Host:Rabbit
Clonality:polyclonal
Clone ID:
Isotype:IgG
Storage:PBS with 0.02% sodium azide and 50% glycerol pH 7.3,-20? for 12 months(Avoid repeated freeze / thaw cycles.)
Background:GLA, also named as Melibiase, Agalsidas and Alpha-galactosidase A, Belongs to the glycosyl hydrolase 27 family. It hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resµLting from the deficient activity of GLA. Enzyme replacement therapy(ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease.
Immunogen:galactosidase, alpha
Synonyms:Alpha galactosidase A, galactosidase, alpha
Observed MW:49 kDa
Uniprot ID:P06280
Reactivity:, Mouse, Rat
Tested Application:ELISA, IHC, IP, WB
Recommended dilution:WB: 1:500-1:5000; IHC: 1:20-1:200; IP: 1:500-1:5000
Gene ID:2717
Research Area:CardiovascµLar, Metabolism, Signal Transduction